Rehabilitación dental de un caso raro de Síndrome de Hallermann-Streiff con Oligodoncia: Reporte de un caso

Autores/as

  • Gül Keskin Assist. Prof. Dr., Department of Pediatric Dentistry, Faculty of Dentistry, Gaziantep University, Gaziantep, Turkey. Autor/a
  • Gün B. Tek Dt., Department of Pediatric Dentistry, Faculty of Dentistry, Faculty of Dentistry, Gaziantep University, Gaziantep, Turkey. Autor/a

DOI:

https://doi.org/10.15517/ijds.2020.42072

Palabras clave:

Anomalías dentales; Síndrome de Hallermann-Streiff; Agenesia dental; Dentición primaria; Aparato nance; Odontología pediátrica.

Resumen

El síndrome de Hallermann-Streiff (HSS) es una discefalia oculomandibulofacial rara con hipotricosis que ocurre como una mutación esporádica. Se caracteriza por hallazgos anormales, especialmente en cabeza y cara. Las anomalías dentales ocurren en 50-80% de los pacientes. En este reporte de caso, se identificaron los hallazgos faciales-orales y las anomalías dentales existentes del síndrome en un paciente masculino de 6 años diagnosticado con HSS. Se informó la rehabilitación dental y un seguimiento de 12 meses del paciente. Cada caso presentado con este síndrome raro puede contribuir a la literatura para determinar el pronóstico de la enfermedad y tomar medidas de protección y prevención.

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Publicado

2026-06-15

Número

Vol. 22 Núm. 3 (2020): Odovtos-International Journal of Dental Sciences

Sección

Reporte de Casos Clinicos

Licencia

Derechos de autor 2020 Gül Keskin, Gün B. Tek (Author)

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