Odovtos - International Journal of Dental Sciences ISSN Impreso: 1659-1046 ISSN electrónico: 2215-3411

OAI: https://revistas.ucr.ac.cr/index.php/Odontos/oai
Síndrome de Papillón-Lefévre. Hiperqueratosis palmo-plantar y enfermedad periodontal agresiva. Caso clínico
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How to Cite

Morales-Vargas, M. (2012). Síndrome de Papillón-Lefévre. Hiperqueratosis palmo-plantar y enfermedad periodontal agresiva. Caso clínico. Odovtos - International Journal of Dental Sciences, (13), 42–47. Retrieved from https://revistas.ucr.ac.cr/index.php/Odontos/article/view/4768

Abstract

The Papillon-Lefévre Syndrome is a rare syndrome that appears in 1 to 4 live births per millon. It is characterized by erythematous palmoplantar hyperkeratosis and agresive periodontal disease that affect both dentition and lead to the total loss of teeth at an in early age. The present article refers to the diagnosis of the syndrome in four sisters residents of Llano Grande de Cartago, the initial treatment took place at the Center of Specialities of Dentistry and Dermatology in the Calderon Guardia Hospital. The early identification of the syndrome plays an important role in prolonging the permanency of the teeth for a longer period in the oral cavity.

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References

Bimstein E. et. al. Periodontitis Asociated with Papillon-Lefévre syndrome. J. Periodontol 1990; 61:373-377.

Bullon P. et. al. Late onset Papillon-Lefévre Syndrome. A chromosomic, neutrophil function and microbiological study. J. Clin. Periodontol. 1993;20:662-667.

Celengil H. et. al. Papillon-Lefévre syndrome. Characterization of peripheral blood and gimgival lymphocytes with monoclonal antibodies. J. Clin Periodontol 1992; 19:392-397.

Christine TN. et. al. Papillon- Lefévre syndrome: Correlating the molecular, cellular, and clinical consequences of cathepsin C/ dipeptidyl pepdidase in humans. J. Immunol. 2004; 173:7277- 7281.

Cortés R. et. al. Hiperqueratosis palmoplantar y enfermedad periodontal severa. Síndrome de Papillón Lefévre. Oral 8 Num. 26. Otoño 2007; 400-403.

De Vree. et. al. Periodontal treatment of rapid progressive periodontitis in 2 sibligs with Papillon Lefévre Syndrom. May 2000; 27:354-360.

Hart T.C. et. al. Mutations of the catepsina C gene are responsible of Papillon- Lefévre Syndrome. J. Med. Genet. December 1999; 36:181-187.

Hattab F. et. al. Papillon- Lefévre syndrome. A review of literature and report of 4 cases. J. Periodontol. 1995; 66:413-420.

Jaiua S.A. et. al. Papillon- Lefévre syndrome: Case report and review of literature. Dermatol Online J 2004; 10:13.

Kleinfelder J. W. et.al. Microbiological ans inmunohistological findings in a patient with Papillon-Lefévre Syndrome. J. Clin. Periodontol. 1996; 23:1032-1038.

Newman et. al. Periodontología Clínica X Edicion. Mc Graw Hill. 2010. 197-197c-198f-236c-298-299-299f.

Sapp J. P. et. al. Patología Oral y Maxilofacial Contemporánea. II Edicion. Editorial Mosby. 2004. 40-41.

Sudhakar S. et. Al. Papillon-Lefévre Syndrome: A Novel Familial Presentation. World Journal Dentistry, Oct-Dec. 2010; 3:209-2012.

The American Academy of Periodontology. Internacional Worshop for a Classification of Periodontal Disease and Conditions. Annals of Periodontology. 1999; 4:1.

Wiebe C. B. et al. Successful periodontal mainteinance of a case with Papillon Lefévre Syndrome. J Periodontol. 2001 jun: 72;6:824-830.

Zhang Y. et al. Evidence of a founder effect effect for four Catepsin C gene mutations in Papillon Lefévre Syndrome patients. J. Med. Gen. February 2001; 38,96-101.

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