Sesión Anatomoclínica I-2018 Autopsia No 38190,Femenina de 57 años con infertilidad primaria, fibrosis pleural y enfermedad renal crónica estadio V secundaria a fibrosis retroperitoneal por enfermedad relacionada con IgG4.

Abstract

A case of a 57-year-old female patient, with history of primary infertility, chronic kidney disease (CKD) stage V secondary to obstructive uropathy; in whom, weight loss studies documented metastasis of poorly differentiated adenocarcinoma without identifying its origin in a retroperitoneal biopsy. The patient evolved insidiously in the course of 16 years. Subsequently, she consulted for progressive dyspnea. Pleural fibrosis and persistently elevated erythrocyte sedimentation rate over the years was documented. The patient progressed to acute
respiratory failure, hydropic decompensation and died. The autopsy showed compatible findings with retroperitoneal fibrosis due to IgG4-related disease