Acidosis tubular renal asociado a Síndrome de Sjögren primario

Abstract

Female patient, 14 years old, previously healthy, with clinical findings of paraparesis and arthralgia. In the laboratory results, she had hypokalemia, metabolic acidosis with normal anion gap and proteinuria. The diagnosis of distal tubular renal acidosis was made, without an underlying cause established in that moment. Symptoms resolved with the administration of potassium citrate. She also had high levels of anti- Ro/SSA and anti-La/SSB autoantibodies, Schirmer´s test was positive, she presented ocular and oral symptoms, therefore a diagnosis of primary Sjögren Syndrome was made.