MÜLLERIAN MALFORMATIONS: ABOUT OHVIRA SYNDROME. CASE REPORTS

Abstract

OHVIRA syndrome (Obstructed Hemivagina and Ipsilateral Renal Anomaly) is characterized by a uterus didelphys, a totally or partially blind hemivagina, and ipsilateral renal agenesis. This article describes three clinical cases of female patients aged 13, 12 and 11, where cyclical cramping abdominal pain was a predominant symptom, mainly associated with a progressively growing abdominal mass and urinary symptoms, irregular menstrual cycles, dysmenorrhea with pain crises that begin with the menstrual period. Other important symptoms were the following: the sensation of pelvic masses, scant and fetid menstrual flow. Likewise, all three patients were found to have ipsilateral renal agenesis. The management was a surgical approach, by means of cystoscopy, vaginoscopy and vaginoplasty with vaginal window of obstructive hemivagina. It should be noted that the surgical intervention was successful and did not present complications. The aim of this study is to give visibility to this syndrome, due to its rare presentation, low incidence and underdiagnosis. Therefore, it is relevant that health personnel become familiar with its different presentations in order to have an early diagnosis and offer timely surgical management, reduce suffering and prevent complications.

Key words: Mullerian Ducts, Solitary Kidney, Uterus, Abnormalities, Multiple. Source: DeCS.